A los diecisiete años desaparecen del EEG las polipuntas y polipunta ondas: a propósito del síndrome de Lance-Adams

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dc.creatorSantoni, Juan R.
dc.creatorSantoni Williams, Carlos Juan
dc.date2020-06-14
dc.date.accessioned2020-09-09T19:44:04Z
dc.date.available2020-09-09T19:44:04Z
dc.descriptionObjective: Unexpected absence of polyspike/polyspike & wave sign (PPW) in the EEG of our 29 and 51-year old published cases of Lance Adams Syndrome (LAS), prompted us to investigate the age when this sign may nearly disappear. This in order of considering it not obligatory for late LAS diagnosis. Methods: Inclusion consisted of a sample of 7137 recordings performed at the Rehabilitation Center and the Universidad Central del Este’s (UCE) teaching clinic (Nervus and Cadwell respectively). Excluded were 198 for unidentifiable indications. PPW was searched in order to study patient’s age, suspected pathology plus gender. Results: PPW was found in 293cases: 4.22% of the total sample: in 275.it occurred before the age of 17 with curve showing an initial tip at nine while between 18 and 65 only 18 cases showed it. Incidentally 14 patients showed Burst suppression or electro-decrement patterns without PPW. The most common indication pathology was Epilepsy followed by learning disability. Finally it was more frequent in 176(63.9%) male vs. 113(36.1%) in female cases: ratio 1.56 to 1. however not significant for the gender ratio in the total EEG sample is 1.55 to 1. Conclusion: PPW nearly disappears after the age of seventeen, perhaps explaining rarity in advanced aged SLA. It is more frequent in Epilepsy EEG indications and in the male.en-US
dc.descriptionObjetivo: la inesperada ausencia del signo de polipunta o de polipunta onda (PPO) en el electroencefalograma (EEG) de dos casos, de 29 y 51 años, respectivamente, del Síndrome Lance Adams (SLA), que hemos visto y publicado con anterioridad, nos motivó a investigar la edad cuando este signo tiende a extinguirse, dejando de ser obligatorio para diagnosticar SLA a pacientes de edad madura. Métodos: de una muestra de 7137 trazados se incluyeron 6939, tras excluir 198 por referimientos no identificables. Estos EEG del Centro de Rehabilitación y el Centro Médico de la Universidad Central del Este (UCE), fueron realizados con electroencefalógrafos Nervus y Cadwell, de manera respectiva. Se revisaron buscando la presencia de PPO para estudiar la edad, la patología sospechada en cada indicación y el género de los pacientes. Resultados: PPO fue encontrada en 293 casos: 4.22 % de la muestra total. En 272 habría ocurrido antes de los 17 años, con la gráfica mostrando una elevación inicial máxima a las nueve. En cambio, de los 18 a los 65 solo apareció la PPO en 18 casos. 14 pacientes mostraron supresión de paroxismo o patrones de electro depresión sin PPO. Conclusión: la polipunta/polipunta onda prácticamente desaparece a los 17 años, a mayor edad, por lo tanto, el signo PPO deja de ser obligatorio para el diagnóstico del SLA en pacientes mayores. Es más frecuente en epilépticos y en varones.es-ES
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dc.identifierhttps://revistas.intec.edu.do/index.php/cisa/article/view/1756
dc.identifier10.22206/cysa.2020.v4i2.pp99-107
dc.identifier.urihttps://repositoriobiblioteca.intec.edu.do/handle/123456789/2770
dc.languagespa
dc.publisherIntituto Tecnológico de Santo Domingo (INTEC)es-ES
dc.relationhttps://revistas.intec.edu.do/index.php/cisa/article/view/1756/2282
dc.relationhttps://revistas.intec.edu.do/index.php/cisa/article/view/1756/2307
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dc.rightsDerechos de autor 2020 Ciencia y Saludes-ES
dc.rightshttps://creativecommons.org/licenses/by-nc-sa/4.0es-ES
dc.sourceScience and Health; Vol 4 No 2 (2020): Science and Health, may-August; 99-107en-US
dc.sourceCiencia y Salud; Vol. 4 Núm. 2 (2020): Ciencia y Salud, mayo-agosto; 99-107es-ES
dc.source2613-8824
dc.source2613-8816
dc.source10.22206/cysa.2020.v4i2
dc.subjectInfantile Myoclonic Epilepsyen-US
dc.subjectBurst suppressionen-US
dc.subjectelectrodecrement patternsen-US
dc.subjectphysio-pathology of Lance Adams Syndromeen-US
dc.subjectepilepsia mioclónica infantiles-ES
dc.subjectsupresión de broteses-ES
dc.subjectpatrón electro depresivoes-ES
dc.subjectfisio patología del síndrome de Lance Adamses-ES
dc.titleAt the seventeen years they disappear from the eeg The little and little waves: About the Lance-Adams syndromeen-US
dc.titleA los diecisiete años desaparecen del EEG las polipuntas y polipunta ondas: a propósito del síndrome de Lance-Adamses-ES
dc.typeinfo:eu-repo/semantics/article
dc.typeinfo:eu-repo/semantics/publishedVersion
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